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Congenital Heart Disease. A Clinical, Pathological, Embryological, and Segmental Analysis

  • Book

  • April 2022
  • Elsevier Health Science
  • ID: 5514735
Authored by the originator of the standard nomenclature for this spectrum of disorders, Congenital Heart Disease: A Clinical, Pathological, Embryological, and Segmental Analysis discusses the history, anatomic features, and physiologic consequences of CHD-in one authoritative resource. The Van Praagh approach to the segmental classification of CHD, developed and implemented by Dr. Richard Van Praagh in the 1960s at Boston Children's Hospital, remains widely used today, facilitating communication among radiologists, cardiologists, surgeons, and pediatricians who are involved in the diagnosis, characterization, and management of this disease. This unique atlas offers complete coverage of the ubiquitous Van Praagh "language� of CHD, including the signs, symptoms, and clinical manifestations of malpositioned, malformed, or absent cardiovascular chambers, vessels, and valves using traditional as well as state-of-the-art technology.
  • Based upon the systematic, widely accepted Van Praagh system of three-part notation used to succinctly describe the visceroatrial situs, the orientation of the ventricular loop, and the position and relation of the great vessels.
  • Demonstrates how the Van Praagh approach facilitates interpreting and reporting findings through cardiac imaging with CT, MR, and ultrasonography, including fetal cardiac imaging.
  • Presents the pathologic anatomy that pediatric and adult cardiologists, radiologists, and echocardiographers need to understand in order to make accurate diagnoses in complex congenital heart disease; as well as the pathologic anatomy that interventionists, pediatric cardiac surgeons, and adult congenital heart surgeons need to know in order to manage their patients successfully.
  • Features more than 550 high-quality images to help you visualize and recognize malformations.
  • Shares the knowledge and expertise of a world-renowned authority on congenital heart disease-a master teacher and the originator of the Van Praagh segmental classification system.
  • Explores the synergy between the various disciplines who manage patient care, including surgeons, radiologists, cardiologists, pathologists, and pediatricians.
  • Enhanced eBook version included with purchase. Your enhanced eBook allows you to access all of the text, figures, and references from the book on a variety of devices.

Table of Contents

HISTORICAL PERSPECTIVE

Brief History of the Cardiovascular System

CARDIOVASCULAR DEVELOPMENT

Embryology and Etiology

ANATOMIC AND DEVELOPMENTAL APPROACH TO DIAGNOSIS

Morphologic Anatomy

Segmental Anatomy

CONGENITAL HEART DISEASE

The Congenital Cardiac Pathology Database

Systemic Venous Anomalies

Pulmonary Venous Anomalies

Cor Triatriatum Sinistrum (Subdivided Left Atrium) and Cor Triatriatum Dextrum (Subdivided Right Atrium)

Interatrial Communications

Juxtaposition of the Atrial Appendages

Common Atrioventricular Canal

Double-outlet and Common-outlet Right Atrium

Tricuspid Valve Anomalies

Mitral Valve Anomalies

Infundibuloarterial Situs Equations: How Normally and Abnormally Related Great Arteries are Built and the Importance of Infundibuloarterial Situs Concordance and Discordance

Ventricular Septal Defects

Single Ventricle

Superoinferior Ventricles

Anomalous ifundibular Muscle Bundles

Tetralogy of Fallot

Absence of the Subpulmonary Infundibulum with its Sequelae has been Misinterpreted as Common Aortopulmonary Trunk that Probably Does Not Exist

Transposition of the Great Arteries

Double-Outlet Right Ventricle

Double-Outlet Left Ventricle

Anatomically Corrected Malposition of the Great Arteries

What Prevents and What Permits the Embryonic Great Arterial Switch?

Infundibulo-Arterial Situs Equations and Analysis

The Cardiac Conduction System

The Heterotxy Syndromes: Asplenia, Polysplenia, and with Normally Formed but Right-Sided Spleen

Authors

Richard Van Praagh Professor Emeritus of Cardiovascular Pathology, Boston Children's Hospital, Harvard University School of Medicine, Boston, Massachusetts. Dr Richard Van Praagh is an internationally renowned pediatric cardiologist with a special interest in cardiac pathology and cardiac embryology. He is originally from Toronto and undertook training with the pathologist Jesse Edwards at the Mayo Clinic before moving to Children's Hospital Boston. Together with his wife Stella he has made seminal contributions to our understanding of the morphology of congenital heart disease. One of his most important contributions was the publication in 1972 of "Segmental approach to diagnosis in congenital heart disease�. Dr. Aldo Castaneda in a recent tribute to Dr. Van Praagh said the following: "Richard impressed me very much, as a renaissance type of individual. He is extremely intelligent and pursues many interests beyond cardiac pathology. His background in philosophy and mathematics, to mention just a few of his many talents, is remarkably broad and deep. His alert and inquisitive mind often races in various direction simultaneously. he is brilliant at conceptualizing embryologic, anatomic sequential developments and deducing their anatomical and functional consequences�.